Rupture of abdominal aortic aneurysm after spine surgery in the patient with Ehlers-Danlos syndrome: A case report.
10.4097/kjae.2010.58.6.555
- Author:
Jung Sik IM
1
;
Yun Hee LIM
;
Jung Sun PARK
;
Sang Seok LEE
;
Kye Min KIM
Author Information
1. Department of Anesthesiology and Pain Medicine, Sanggye Paik Hospital, Inje University, Seoul, Korea. painfree@paik.ac.kr
- Publication Type:Case Report
- Keywords:
Abdominal aorta rupture;
Ehlers-Danlos syndrome;
Hemorrhage
- MeSH:
Adolescent;
Aneurysm, False;
Aortic Aneurysm, Abdominal;
Aortic Rupture;
Cardiovascular System;
Congenital Abnormalities;
Connective Tissue;
Ehlers-Danlos Syndrome;
Hematoma;
Hemorrhage;
Humans;
Joints;
Rupture;
Skin;
Spine
- From:Korean Journal of Anesthesiology
2010;58(6):555-559
- CountryRepublic of Korea
- Language:English
-
Abstract:
Ehlers-Danlos syndrome (EDS) is a rare inherited disorder of the connective tissue that is characterized by hyperextensible skin, hypermobile joints and abnormalities of the cardiovascular system. A 15-year-old girl with Ehlers-Danlos syndrome underwent thoracolumbar surgery for deformity correction. After surgery, an abdominal aortic rupture occurred, and she complained of abdominal distension had an abdominal circumference of 80 cm. Abdominal computed tomography revealed a pseudoaneurysm and a large hematoma at the retroperitoneum. She died of a massive hemorrhage during subsequent abdominal aortic surgery.
