A Case of Linear and Whorled Nevoid Hypermelanosis.
- Author:
Tuk Woo LIM
1
;
Mu Hyoung LEE
Author Information
1. Department of Dermatology, College of Medicine, Kyung Hee University, Seoul, Korea. tukwoo@lycos.co.kr
- Publication Type:Case Report
- Keywords:
Linear and whorled nevoid hypermelanosis;
Blaschko's line
- MeSH:
Congenital Abnormalities;
Congenital, Hereditary, and Neonatal Diseases and Abnormalities;
Humans;
Hyperpigmentation*;
Infant;
Male;
Mosaicism;
Parturition;
Rare Diseases
- From:Korean Journal of Dermatology
2001;39(4):486-488
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Linear and whorled nevoid hypermelanosis(LWNH) is a congenital disorder which was first described by Kalter in 1988 and is characterized by asymmetrically distributed linear and whorled hyperpigmentation following Blaschko's lines. It usually appears at birth or during the first weeks of life and is rarely associated with various congenital defects. Its pathogenesis is not well known, but developmental somatic mosaicism appears the most likely cause. It is probably not a rare disease, but not well recognized or is confused with other entities. Herein, we report a typical case of LWNH in 9 month-old boy.