Surgical Treatment of the Craniofacial Dysostoses-Crouzon's Disease.
- Author:
Joon Ki KANG
1
;
Jin Un SONG
;
Jin Chul KIM
;
Poong LIM
Author Information
1. Department of Neurosurgery, Catholic University Medical Colelge, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
Craniofacial;
dysostoses;
Crouzon's disease;
Middle facial mass;
Total osteotomy
- MeSH:
Adolescent;
Congenital Abnormalities;
Craniofacial Dysostosis;
Craniosynostoses;
Dental Occlusion;
Dysostoses;
Facial Bones;
Humans;
Male;
Maxilla;
Orbit;
Osteotomy;
Skull Base
- From:Journal of Korean Neurosurgical Society
1987;16(1):289-296
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Craniofacial dysostoses(Crouzon's disease) are characterized by cranial and facial deformities but the relationship between the craniosynostosis and facial deformities has not been clearly established. However, we believe that certain facial hypoplasias are comparable in nature with craniostenosis. Our objective in treatment of the Crouzon's disease is to achieve a postero-anterior movement of the whole facial mass, with the double aim of establishing normal dental occlusion and of increasing orbital capacity. The method we describe uses Tessier's basic procedures for surgical correction of the Crouzon's diseases patient who was 16 year-old boy. It would appear that the best treatment of these requires a radical and total osteostomy of the middle third of the face, to permit complete repositioning of the involved segment. These total osteotomies frequently include the creation of a line of separation between the anterior cranial base above and the facial bone below and also between the pterygoid processes behind and the maxilla anteriorly. Thus one is detaching the face from the cranial base. The authors described the surgical management of the Crouzon's disease and discussed the warning points of intraoperative technique in correction of the craniofacial dysostosis.
