Retiform hemangioendothelioma in the infratemporal fossa and buccal area: a case report and literature review.
10.5125/jkaoms.2016.42.5.307
- Author:
Il Kyu KIM
1
;
Hyun Young CHO
;
Bum Sang JUNG
;
Sang Pill PAE
;
Hyun Woo CHO
;
Ji Hoon SEO
;
Seung Hoon PARK
Author Information
1. Division of Oral and Maxillofacial Surgery, Department of Dentistry, Inha University School of Medicine, Incheon, Korea. kik@inha.ac.kr
- Publication Type:Case Report
- Keywords:
Retiform hemangioendothelioma;
Infratemporal fossa;
Le Fort osteotomy;
Residual neoplasm
- MeSH:
Adolescent;
Cavernous Sinus;
Diagnosis;
Follow-Up Studies;
Hemangioendothelioma*;
Humans;
Male;
Neoplasm Metastasis;
Neoplasm, Residual;
Orbit;
Osteotomy;
Osteotomy, Le Fort;
Sphenoid Bone
- From:Journal of the Korean Association of Oral and Maxillofacial Surgeons
2016;42(5):307-314
- CountryRepublic of Korea
- Language:English
-
Abstract:
We report a case of retiform hemangioendothelioma (RH) located in the infratemporal fossa and buccal area in a 13-year-old Korean boy. The tumor originated from the sphenoid bone of the infratemporal fossa area and spread into the cavernous sinus, orbital apex, and retro-nasal area with bone destruction of the pterygoid process. Tumor resection was conducted via Le Fort I osteotomy and partial maxillectomy to approach the infratemporal fossa and retro-nasal area. The diagnosis of RH was confirmed after surgery. In the presented patient, surgical excision was incomplete, and close follow-up was performed. There was no evidence of expansion or metastasis of the residual tumor in the 8 years after surgery. In cases of residual RH with low likelihood of expansion and metastasis, even though RH is an intermediate malignancy, close follow-up can be the appropriate treatment choice over additional aggressive therapy. To date, 29 papers and 48 RH cases have been reported, including this case. This case is the second reported RH case presenting as primary bone tumor and the first case originating in the oromaxillofacial area.