3 Cases of Mobius Syndrome.
- Author:
Dong Su KIM
1
;
Jun HUR
;
In Gun WON
Author Information
1. Department of Ophthalmology, College of Medicine, Inje University, Pusan, Korea.
- Publication Type:Original Article
- Keywords:
Mobius syndrome;
Esodeviation;
Medial rectus recession;
Lateral rectus resection
- MeSH:
Amputation;
Atrophy;
Clubfoot;
Cranial Nerves;
Esotropia;
Extremities;
Facial Paralysis;
Mobius Syndrome*;
Paralysis;
Tongue
- From:Journal of the Korean Ophthalmological Society
1997;38(5):890-896
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Mobius syndrome is a rare congenital disease characterized by unilateral or bilateral limitation of abduction and facial palsy due to the 6th and 7th cranial nerve paralysis. In addition, it may be associated with limb anomalies and other cranial nerve paralysis. We experienced three cases of Mobius syndrome characterized by esodeviation associated with bilateral limitation of abduction, bilateral facial atroph, tongue atrophy, congenital amputation of limb, and congenital clubfoot. We performed a large amount of bilateral medial rectus recession and unilateral lateral rectus resection, and obtained cosmetically successful results that orthophoric or less than 10 prism diopter of esotropia in primary postition, but mild limitation of adduction was observed as a complication.
