Idiopathic Unilateral Retroperitoneal Fibrosis Diagnosed in a Patient with Normal Renal Function and Left Flank Pain.
- Author:
Moon Hyoung LEE
1
;
Kyoung Hyoub MOON
;
Beom KIM
;
Dong young LEE
;
Won Keun SI
;
Jin Ah HWANG
;
Bo Kyoung CHOI
;
Kang hum SEO
Author Information
1. Department of Internal Medicine, Seoul Veterans Hospital, Seoul, Korea. purejuliet@paran.com
- Publication Type:Case Report
- Keywords:
Unilateral;
Retroperitoneal fibrosis;
Steroid
- MeSH:
Aorta, Abdominal;
Atherosclerosis;
Autoimmune Diseases;
Flank Pain;
Humans;
Hydronephrosis;
Iliac Artery;
Oliguria;
Prednisolone;
Retroperitoneal Fibrosis;
Uremia;
Ureter
- From:Korean Journal of Nephrology
2011;30(3):325-328
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Retroperitoneal fibrosis is a disease characterized by proliferation of fibro-inflammatory tissue, which mainly encloses the abdominal aorta, iliac arteries and (enlarges to the retroperitoneum to surrounds) ureters. Two leading pathogenesis are an exacerbated local inflammatory reaction to aortic atherosclerosis and a manifestation of systemic autoimmune disease. Because of insidious disease course, most cases are diagnosed late when bilateral urinary obstruction caused oliguria and symptoms related to uremia. In this case, the patient complained left flank pain which might have been caused by left ureter stone, but through abdominal CT scan, the patient was diagnosed as left unilateral retroperitoneal fibrosis. Abdominal CT scan showed encircling mass around abdominal aorta and left ureter with hydronephrosis. The patient had no underlying disease and didn't take any medication; she was diagnosed as idiopathic unilateral retroperitoneal fibrosis and started prednisolone, 40 mg daily. Three months have passed since the therapy was started; most fibrous tissue was disappeared, hydronephrosis was resolved and flank pain was relieved.
