A Case of Isolated Right Pulmonary Artery Agenesis.
10.4046/trd.2004.57.5.489
- Author:
Do Youn KIM
1
;
Jae Sung LEE
;
Young KIM
;
Yoon Soo CHANG
;
Hyung Jung KIM
;
Tae Hoon KIM
;
Chul Min AHN
Author Information
1. Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea. Ahnswine@naver.com
- Publication Type:Case Report
- Keywords:
Isolated right Pulmonary artery agenesis
- MeSH:
Angiography;
Cardiovascular Abnormalities;
Dyspnea;
Female;
Humans;
Middle Aged;
Perfusion;
Pulmonary Artery*;
Tetralogy of Fallot;
Thorax
- From:Tuberculosis and Respiratory Diseases
2004;57(5):489-493
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Unilateral pulmonary artery agenesis is a rare congenital anomaly usually associated with other cardiovascular anomalies such as tetralogy of Fallot or septal defect. Unilateral pulmonary artery agenesis without other coexisting cardiovascular abnormality (isolated unilateral pulmonary artery) is extremely rare and often asymptomatic until adulthood. In these patients, diagnostic clue is found in a plain chest roentgenogram, showing a hyperlucent contracted hemithorax. We have recently experienced a case of isolated right pulmonary artery agenesis, which was diagnosed by chest dynamic CT, perfusion scan, echocardiogram and 3-dimensional reconstruction cardiac CT angiography in a 50-year old female who had suffered from mild dyspnea on exertion and improved with conservative treatment. We report this case with a brief review of the relevant literature.
