Juvenile Paget's Disease with Paranasal Sinus Aplasia.
- Author:
Ki Beom BAE
1
;
Jae Hwan KWON
;
Young Ho KIM
;
Tae Young JUNG
;
Joong Hwan CHO
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, Maryknoll Medical Center, Busan, Korea. entkwon@hanmail.net
- Publication Type:Case Report
- Keywords:
Paget disease of bone;
Osteitis deformans;
Paranasal sinuses;
Paranasal sinus neoplasms
- MeSH:
Alkaline Phosphatase;
Asian Continental Ancestry Group;
Ethmoid Sinus;
Humans;
Male;
Osteitis Deformans;
Paranasal Sinus Neoplasms;
Paranasal Sinuses;
Preschool Child
- From:Clinical and Experimental Otorhinolaryngology
2008;1(4):224-226
- CountryRepublic of Korea
- Language:English
-
Abstract:
Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
