A case of hepatopulmonary syndrome in a child with fatty liver disease secondary to hypopituitarism after craniopharyngioma resection.
10.3345/kjp.2007.50.8.794
- Author:
Sun Ju IM
1
;
Hyoung Doo LEE
;
Jae Hong PARK
;
Hee Ju PARK
Author Information
1. Department of Pediatrics, College of Medicine, Pusan National University, Busan, Korea. phj7294@hanmail.net
- Publication Type:Case Report
- Keywords:
Hepatopulmonary syndrome;
Fatty liver disease;
Hypopituitarism;
Craniopharyngioma
- MeSH:
Adult;
Child*;
Craniopharyngioma*;
Dilatation;
Fatty Liver*;
Hepatopulmonary Syndrome*;
Humans;
Hypopituitarism*;
Incidence;
Liver;
Liver Diseases;
Oxygen;
Pituitary Neoplasms
- From:Korean Journal of Pediatrics
2007;50(8):794-798
- CountryRepublic of Korea
- Language:English
-
Abstract:
Hepatopulmonary syndrome is a triad that includes: hepatic dysfunction, intrapulmonary vascular dilatation and abnormal arterial oxygenation. The incidence of intrapulmonary vascular dilatations, in adults with end-stage liver disease, has been reported to be 13% to 47%, however the incidence in children is unclear and the cases in Korean children have never been reported. The hepatopulmonary syndrome may occur as a result of chronic liver disease following nonalcoholic steatohepatitis in children with hypothalamic or pituitary dysfunction. We report a case of hepatopulmonary syndrome in a 13-year- old child who had rapidly progressive liver dysfunction secondary to panhypopituitarism after craniopharyngioma resection. Careful monitoring and treatment of endocrine abnormalities and metabolic status, as well as liver function, are required in all children undergoing pituitary tumor resection.
