Hydrocephalus In Achondroplasia: Case Report.
- Author:
Keun Bae RHA
1
;
Chul Koo JUNG
;
Tai Hoon CHO
;
Un Sung CHOI
;
Dal Soo KIM
Author Information
1. Department of Neurosurgery, Capital Armed Forces General Hospital, Seoul, Korea.
- Publication Type:Original Article
- Keywords:
Hydrocephalus;
Achondroplasia;
Premature synostosis
- MeSH:
Absorption;
Achondroplasia*;
Constriction, Pathologic;
Foramen Magnum;
Humans;
Hydrocephalus*;
Lateral Ventricles;
Skull;
Spinal Cord;
Spine;
Superior Sagittal Sinus;
Synostosis
- From:Journal of Korean Neurosurgical Society
1982;11(2):225-229
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Major neurological features of achondroplasia are attributed to premature synostoses of the pedicles of the vertebrae and of the base of the skull producing obstruction of the ventricular fluid circulation or compression of the medulla and spinal cord. Significant hydrocephalus is due to the obstruction of the cerebrosspinal fluid pathways at the level of the foramen magnum or the disturbance of CSF absorption caused by increased superior sagittal sinus pressure. In generally, the hydrocephalus in achondroplasia is of the communicating type in the pattern, so the CSF diversionary shunt may not be indicate. But, shunting procedures may be needed in patients who showed signs of severe IICP such as bulging fontanels and enlarged lateral ventricle. In this case, we experienced that the hydrocephalus in achondroplasia is prosorption following the stenosis of the foramen magnum and increased superior sagittal sinus pressure.
