A giant retroperitoneal lymphangioma in a patient with neurofibromatosis type 1.
10.4174/jkss.2011.80.Suppl1.S43
- Author:
Jeong Ho KIM
;
Min Ok KIM
;
Young Jin CHOI
;
Hyun Young HAN
;
Kang Seo PARK
;
Byung Sun CHO
;
Dong Wook KANG
- Publication Type:Case Report
- Keywords:
Lymphangioma;
Retroperitoneal neoplasms;
Neurofibromatosis 1
- MeSH:
Brain;
Gallbladder;
Head;
Humans;
Kidney;
Liver;
Lung;
Lymphangioma;
Lymphatic System;
Mesentery;
Neck;
Nerve Tissue;
Neurofibromatoses;
Neurofibromatosis 1;
Pericardium;
Peripheral Nerves;
Pleura;
Retroperitoneal Neoplasms;
Skin;
Skin Abnormalities;
Spinal Cord;
Subcutaneous Tissue
- From:Journal of the Korean Surgical Society
2011;80(Suppl 1):S43-S46
- CountryRepublic of Korea
- Language:English
-
Abstract:
Neurofibromatosis type 1 (NF-1) is a genetically inherited disorder that may cause skin abnormalities and tumors that form on nerve tissues. These tumors can be small or large and can occur anywhere in the body, including the brain, spinal cord, or other peripheral nerves. Retroperitoneal lymphangiomas are very rare benign malformations of the lymphatic system. About 95% lymphangiomas occur in the skin and the subcutaneous tissues of the head, neck and axillary region and the remaining 5% appear in other parts of the body such as lungs, pleura, pericardium, liver, gallbladder, kidney, and the mesentery. Herein, we report the case of a giant retroperitoneal lymphangioma in a patient with NF-1 with a review of the literature.
