Rectal Involvement of Klippel-Trenaunay Syndrome.
10.3393/jksc.2009.25.1.52
- Author:
Seong Hui CHEON
1
;
Suk Hwan LEE
;
Eung Bum PARK
Author Information
1. Department of Surgery, Ewha Womans University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Rectal bleeding;
Klippel-Trenaunay syndrome;
Coloanal anastomosis
- MeSH:
Anemia;
Capillaries;
Congenital, Hereditary, and Neonatal Diseases and Abnormalities;
Emergencies;
Gastrointestinal Hemorrhage;
Hemorrhage;
Humans;
Klippel-Trenaunay-Weber Syndrome
- From:Journal of the Korean Society of Coloproctology
2009;25(1):52-55
- CountryRepublic of Korea
- Language:English
-
Abstract:
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder and is essentially a disorder of capillary, venous, and lymphatic malformations. Hematochezia is the most common symptom associated with intestinal hemangiomatosis and remains one of the life-threatening emergencies in KTS. We reported one patient of KTS presented with rectal bleeding and severe anemia who was successfully managed by sphincter-saving operation.
