A Case of Tuberous Sclerosis Complex Developing with Subependymal Giant-Cell Astrocytoma and Hydrocephalus.
- Author:
Ki Hyun CHUNG
1
;
Wan Sub KIM
Author Information
1. Department of Pediatrics, Presbyterian Medical Center, Chonju, Korea.
- Publication Type:Case Report
- Keywords:
Subependymal giant-cell astrocytoma;
Tuberous Sclerosis Complex
- MeSH:
Astrocytoma*;
Brain;
Cerebral Ventricles;
Child;
Diagnosis;
Glioma;
Humans;
Hydrocephalus*;
Lateral Ventricles;
Magnetic Resonance Imaging;
Male;
Tuberous Sclerosis*
- From:Journal of the Korean Pediatric Society
1996;39(2):280-286
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The subependymal giant-cell astrocytoma, a key feature of the tuberous sclerosis complex, has been reported in patients without obvious features of this condition. The tumor is a rare cerebral glioma that characteristically arise in the wall of lateral ventricle and as an intraventricular mass, causing hydrocephalus by obstruction of the foramen of Monro. We experienced a case of tuberous sclerosis in 9-year-old male patient who presented typical clinical manifestations and cortical tuber, subependymal giant-cell astrocytoma developing with hydrocephalus. Diagnosis was confirmed by brain CT and MRI. We applied surgical resection to remove the mass. Brief review and related literatures were also presented.
