Two cases of Dyke-Davidoff-Masson syndrome.
- Author:
Dong Gun PARK
;
Ji Hee PARK
;
Kee Hwan YOO
;
Ji Tae CHOUNG
;
Chang Sung SON
;
Young Chang TOCKGO
- Publication Type:Original Article
- Keywords:
Cerebral hemiatrophy;
Hemiparesis
- MeSH:
Brain;
Dilatation;
Female;
Humans;
Intellectual Disability;
Lateral Ventricles;
Male;
Paresis;
Pediatrics;
Petrous Bone;
Seizures;
Temporal Bone;
Tomography, X-Ray Computed
- From:Journal of the Korean Pediatric Society
1993;36(6):865-869
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Dyke-Davidoff-Masson syndrome is a rare disorder which developed hemiatrophy of brain, enlargement of ventricles and prominent pneumatization of petrous pyramid of the temporal bone. It manifests hemiparesis, varying type seizure, and mental retardation. We experienced two cases of Dyke-avidoff-Masson Syndrome, in a 6/12 year-old boy and a 1, 10/12 year-old girl who were admitted to our department of pediatrics, because of convulsion and hemiparesis The brain CT scan showed marked dilatation of lateral ventricle, prominent sylvian fissure and cortical sulci. So we report two cases of Dyke-Davidoff-Masson syndrome with review of literature.
