A Case of Immunoglobulin G4-Related Tubulointerstitial Nephritis with Extrarenal Involvement.
- Author:
Jinhee AHN
1
;
Sang Heon SONG
;
Dong Uk KIM
;
Hyun Ju CHOI
;
Joo Wan SEO
;
Sang Bo OH
;
Harin RHEE
;
Hee Sun LEE
;
Ihm Soo KWAK
Author Information
1. Department of Internal Medicine, Pusan National University Hospital, Busan, Republic of Korea. shsong@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Immunoglobulin;
Cholangitis;
sclerosing;
Sialadenitis;
Tubulointerstitial nephritis
- MeSH:
Bile Ducts;
Cholangitis;
Cholangitis, Sclerosing;
Early Diagnosis;
Humans;
Immunoglobulins;
Kidney;
Lung;
Male;
Middle Aged;
Nephritis, Interstitial;
Pancreas;
Prednisolone;
Prognosis;
Prostate;
Salivary Glands;
Sialadenitis;
Steroids;
Urinary Bladder
- From:Korean Journal of Nephrology
2011;30(6):656-660
- CountryRepublic of Korea
- Language:English
-
Abstract:
Immunoglobulin G4-related sclerosing disease is a novel clinicopathological disease entity known to involve various organs including the pancreas, bile ducts, gall bladder, retroperitoneum, kidney, salivary gland, lung and prostate. The most common organ involved is the pancreas and cases without pancreatic involvement are uncommon. Positive response to steroids is an important characteristic of this disease and this enables early diagnosis, which is required for good prognosis. We demonstrate a case of immunoglobulin G4-related tubulointerstitial nephritis in a 59-year-old male accompanied by sclerosing cholangitis and sialadenitis without any evidence of pancreatic infiltration. The patient was treated with prednisolone and was fully recovered in 6 months.
