Congenital Onychodysplasia of the Index Fingers with a Y-shaped Bifurcation of the Distal Phalanx.
- Author:
Hee Joo KIM
1
;
Kyung Goo LEE
;
Sang Min YI
;
Jae Hwan KIM
;
Jae Eun CHOI
;
Sang Wook SON
;
Il Hwan KIM
Author Information
1. Department of Dermatology, College of Medicine, Korea University, Seoul, Korea. kumcihk@korea.ac.kr
- Publication Type:Case Report
- Keywords:
Congenital onychodysplasia of the index fingers;
Iso and Kikuchi syndrome
- MeSH:
Arteries;
Congenital, Hereditary, and Neonatal Diseases and Abnormalities;
Fingers;
Ischemia;
Nails
- From:Korean Journal of Dermatology
2010;48(8):729-731
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital onychodysplasia of the index fingers (COIF, Iso and Kikuchi syndrome) is a congenital disorder characterized by various forms of nail dysplasias mainly-involving the index fingers. Its etiopathogenesis is still unknown, but ischemia of the palmar digital arteries has been suggested to play a role in this disorder. Although not specific to it, a Y-shaped bifurcation of the distal affected phalanx is a characteristic finding of this syndrome. In this review, we report a case of COIF who presented with bilateral micronychia with a Y-shaped bifurcation of the distal phalanx.
