Anesthetic Management in a Patient with Charcot-Marie-Tooth Disease: A case report.
10.4097/kjae.2006.50.3.341
- Author:
Eun Sung KIM
1
;
Hae Wone CHANG
;
Won Jung HWANG
;
Yoon Ki LEE
Author Information
1. Department of Anesthesiology and Pain Medicine, College of Medicine, The Catholic University of Korea, Seoul, Korea. yklee@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Charcot-Marie-Tooth disease;
train-of-four (TOF) response;
vecuronium
- MeSH:
Adult;
Anesthesia;
Anesthesia, Epidural;
Anesthesia, General;
Anesthetics;
Body Temperature;
Cesarean Section;
Charcot-Marie-Tooth Disease*;
Enflurane;
Female;
Humans;
Leiomyoma;
Pregnancy;
Propofol;
Reference Values;
Vecuronium Bromide
- From:Korean Journal of Anesthesiology
2006;50(3):341-345
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 35-year old woman was scheduled to undergo a total hystectomy due to uterine myoma. She had been diagnosed with Charcot-Marie-Tooth disease 2 years ago. In addition, she had previously received a Cesarean section under epidural anesthesia 10 years ago and reported a prolonged motor blockade at that time. General anesthesia was induced with propofol 120 mg in a divided dose and the intubating condition was achieved with vecuronium 3 mg. Anesthesia was maintained with 1.5-2.5% enflurane with air and O2. During surgery, the body temperature and end tidal concentration of CO2 were maintained within the normal range. Despite the continuous monitoring of the train-of-four (TOF) response, no more muscle relaxants were required during surgery and the patient recovered without a delay in awakening. In the management of patients with Charcot-Marie-Tooth disease, it is desirable to evaluate the patient carefully, select the appropriate anesthetics and adjust the dosage of the drug according to the patients requirements.
