A Case of Infantile Myofibromatosis.
- Author:
Won Ho KIM
1
;
Jeong Ho RYU
;
Kwang Ho KIM
;
Kwang Joong KIM
Author Information
1. Department of Dermatology, College of Medicine, Hallym University, Anyang, Korea. lucki96@hanmail.net
- Publication Type:Case Report
- Keywords:
Infantile myofibromatosis;
Sole
- MeSH:
Dermis;
Female;
Fibroma;
Humans;
Myofibromatosis*;
Physical Examination;
Prognosis;
Skin;
Viscera
- From:Korean Journal of Dermatology
2004;42(4):469-471
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Infantile myofibromatosis is the most common of the juvenile fibromatoses and an unusual mesenchymal disorder characterized by the proliferation of tumors in the skin, muscle, bone and viscera. There are two forms of the disease: solitary and multicentric. A benign course with spontaneous regression is seen in most patients, but poor prognosis can be associated with the multicentric form, in which visceral organs may be involved. It usually presents in early childhood. We report a case of infantile myofibromatosis arising in the left sole of a female new born. Physical examination showed a firm, red colored 2x4cm sized tumor. Histological examination revealed a spindle cell tumor in the dermis with fascicles of plump spindle cells with a whorled arrangement.
