A Case of Nevus Unius Lateris with Retroperitoneal Leiomyosatcoma.
- Author:
Chung Won KIM
;
Kang Woo LEE
;
Won HOUH
- Publication Type:Original Article
- MeSH:
Cafe-au-Lait Spots;
Congenital Abnormalities;
Humans;
Leiomyosarcoma;
Male;
Nevus*;
Parents;
Parturition;
Pregnancy;
Skin
- From:Korean Journal of Dermatology
1977;15(4):471-475
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Epidermal nevus syndrome, which used to combine congenital abnormalities of the central nervous and skeletal system and others, are not ingrequently encountered. Until now fer cases of epidermal nevus with intemal malignancy were reported in the literatures, Since the report on this epidermal nevus associated with intemal malignancy, the newer finding was interested by dermatologist. A case of 3 and half months old boy who had nevus unius lateris and retroperitoneal leiomyosarcoma since at birth was seen at St. Mart's Hospital. He did not mongolian and cafe au lait spots on the vack which seemed to be a characteristicaign of epidermal nevus syndrome, His developmenta percmtile was 25 of his matched age group. He was bome with spontaneous normal delibery in the hospital. His parents were relatively healthy and his morher had no history of any kind of medicine taken during the pregnancy. There were no family history of epidermal nevuys like skin lesions and hereditary disorders.