A Case of Pulmonary Lymphangioleiomyomatosjs Associated with Thberous Sclerosis and Renal Angiomyolipoma.
10.4046/trd.1997.44.5.1184
- Author:
Jung Min BAIK
1
;
Han Ki HONG
;
Young Bae OH
;
Sang Moo LEE
;
Man Sil PARK
;
Tak Keun YOO
;
Eun Joo KO
;
Eun Kyung KIM
Author Information
1. Department of Internal Medical Nowon Eulji Medical Center, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Tuberous sclerosis;
Pulmonary lymphangioleiomyomatosis
- MeSH:
Adult;
Angiomyolipoma*;
Biopsy;
Cough;
Dyspnea;
Female;
Humans;
Kidney;
Lung;
Sclerosis*;
Thorax;
Tomography, X-Ray Computed;
Tuberous Sclerosis
- From:Tuberculosis and Respiratory Diseases
1997;44(5):1184-1193
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Lymphangioleiomyomatosis(LAM) is rare and essentially limited to women in the reproductive ages. A 39-year-old female was admitted due to progressive exerUional dyspnea and intermittent productive cough. Chest PA showed marked hyperinflation of the lung associated with a diffuse reticulo-nodular pattern. High resolution CT scan of the thorax demonstrated that diffusely scattered thin-walled cysts were distributed throughout the bilateral lung fields. Abdominal CT scan showed variable sized multiple angiomyolipoma of both kidney. By open lung biopsy, she was diagnosed as pulmonary LAM associated with Tuberous sclerosis and renal Angiomyolipoma. We present the case and discuss the connection between pulmonary LAM and Tuberous sclerosis.
