A Case of Fahr's Disease Presenting with Frontal Lobe Dysfunction.
- Author:
Jae Hyeok HEO
1
;
Yoon Jae CHOI
;
Kyoung Min LEE
Author Information
1. Department of Neurology, Seoul National University Hospital, Seoul, Korea. kminlee@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Fahr's disease;
Frontal function
- MeSH:
Basal Ganglia;
Cerebellum;
Cerebrum;
Dyskinesias;
Frontal Lobe*;
Humans;
Middle Aged;
Mood Disorders;
Movement Disorders;
Neuroimaging;
Neurologic Examination
- From:Journal of the Korean Neurological Association
2007;25(4):549-552
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Bilateral calcifications of the basal ganglia, the thalami, the dentate nuclei of the cerebellum, and the white matter of the cerebral hemisphere characterize Fahr's disease. The common clinical manifestations of the disease are movement disorders accompanied by cognitive impairment and mood disorder. Herein we report a case of Fahr's disease with atypical clinical manifestations. The patient was a 48 year-old man who presented with behavioral changes. His neurological examination showed no focal neurological deficits except for frontal dysfunctions. Abnormal involuntary movement was absent. Neuroimaging work-ups were compatible with Fahr's disease.
