Unresectable Desmoid Tumor Developing after Surgery of F.A.P Case report.
- Author:
Hyeon Serk LEE
;
Hae Myung JEON
;
Seong Taek OK
;
Jeong Soo KIM
;
Eun Jung LEE
;
Jae Sung KIM
- Publication Type:Case Report
- Keywords:
Desmoid tumor;
F.A.P (Familial adenomatous polyposis)
- MeSH:
Deception;
Epidermal Cyst;
Fibroma;
Fibromatosis, Aggressive*;
Humans;
Incidence;
Intestinal Polyposis;
Osteoma;
Recurrence
- From:Journal of the Korean Society of Coloproctology
1998;14(2):323-329
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Desmoid tumors are defined as aggressive overgrowth of fibrous sheets and musculoaponeurotic structures. Although desmoid tumors are generally known as a benign neoplasm, it's aggresive local invasiveness and frequent recurrence indicate it's position lying between the benign and malignancy. The association of desmoid tumor and familial adenomtous polyposis(FAP) was first made in 1923 by Nichols. In 1951, Gardner reported the familial occurrence of intestinal polyposis, osteomas, fibromas, and epidermal or sebaceous cyst. Desmoid tumors are common in patients with FAP and Occur in 3.5~29% of patients with FAP whereas the incidence in the gerenal population is 2~5/1,000,000 person years. Surgical resection of desmoids in patients with FAP has been controversial because unresectability and recurrence are more common than cure. Palliative and curative resections have a high morbidity. Surgery should be reserved for those patients with symptomatic mesenteric desmoids. If a small mesenteric desmoid is encountered incidentally and is easily resectable, it should be resected. If surgery has been less than satisfactory in the treatment of these patients, several different medical approaches can be combined with or without surgical resection with mixed result. Authors report a case of unresectable mesenteric desmoid tumor, developing after surgery of FAP and literatures were reviewed
