Hailey-Hailey Disease with a Family Histroy and Unique Nail Lesions.
10.5021/ad.1999.11.4.271
- Author:
Min Ja JUNG
;
Sang Jun LEE
;
Yoon Whoa CHO
;
Jee Yoon HAN
;
Kye Yong SONG
- Publication Type:Original Article
- Keywords:
Family history;
Hailey-hailey disease;
Unique nail lesions
- MeSH:
Acantholysis;
Axilla;
Blister;
Friction;
Groin;
Humans;
Nails;
Neck;
Pemphigus, Benign Familial*;
Skin
- From:Annals of Dermatology
1999;11(4):271-275
- CountryRepublic of Korea
- Language:English
-
Abstract:
Hailey-Hailey disease(benign familial chronic pemphigus) is a rare autosomal dominant disorder characterized by blisters at sites of friction such as the neck, axillae and groin which are caused by suprabasal epidermal acantholysis. We report two cases of Hailey-Hailey disease in the one family. One of the two cases has asymptomatic multiple longitudinal white bands in the fingernails associated with typical skin lesions. The nail lesions have not been described until reported by Burge in 1992 and it may be a characteristic finding in Hailey-Hailey disease.
