Two Cases of Infantile Intra-abdominal Inflammatory Myofibroblastic Tumor.
10.5223/pghn.2014.17.2.116
- Author:
Soo Hong KIM
1
;
Yong Hoon CHO
;
Hae Young KIM
Author Information
1. Division of Pediatric Surgery, Department of Surgery, Pusan National University Children's Hospital, Pusan National University School of Medicine, Yangsan, Korea. choyh70@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Inflammatory myofibroblastic tumor;
Intraabdominal;
Infant
- MeSH:
Child;
Humans;
Infant;
Liver;
Male;
Mesentery;
Myofibroblasts*;
Neoplasm Metastasis;
Neoplastic Processes;
Prevalence;
Recurrence;
Thoracic Cavity;
Young Adult
- From:Pediatric Gastroenterology, Hepatology & Nutrition
2014;17(2):116-120
- CountryRepublic of Korea
- Language:English
-
Abstract:
Inflammatory myofibroblastic tumor (IMT) is rare mesenchymal solid tumor that consists of proliferating myofibroblasts with an inflammatory infiltrate background. It has a very low prevalence in infants and occurs mainly in children and young adults. IMT are mainly located in the thoracic cavity, but intra-abdominal lesions are rare. IMT can exhibit locally aggressive neoplastic processes and metastases similar to malignancies, so, have clinical importance. Herein, we describe two infantile intra-abdominal IMT cases presenting with incidentally found palpable abdominal mass. A 4-month-old male infant had IMT at the ileal mesentery and a 5-month-old male infant had IMT at liver. Both cases were successfully treated by complete surgical resection without complication or recurrence. Considering the biological behavior of the intermediate type of neoplasm in IMT, we expect good survivals when achieving appropriate surgical resection without adjuvant therapy in infantile intra-abdominal IMT.