A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement.
10.5090/kjtcs.2015.48.1.90
- Author:
Bong Jun KIM
1
;
Tae Hoon KIM
;
Do Jung KIM
;
Dongsub NOH
;
Seok Jin HAAM
;
Sungsoo LEE
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine, Korea. CHESTLEE@yuhs.ac
- Publication Type:Case Report
- Keywords:
Sternum;
Gorham-Stout Syndrome
- MeSH:
Adolescent;
Bone Resorption;
Chylothorax;
Humans;
Male;
Osteolysis;
Prognosis;
Rare Diseases;
Respiratory Insufficiency;
Ribs;
Skeleton;
Sternum;
Thorax
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2015;48(1):90-94
- CountryRepublic of Korea
- Language:English
-
Abstract:
Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.
