Mid-term Results of Neonatal Surgical Management of Pulmonary Atresia with Intact Ventricular Septum.
- Author:
Jae Gun KWAK
1
;
Woong Han KIM
;
Dong Jin KIM
;
Chang Ha LEE
;
Jeong Ryul LEE
;
Yong Jin KIM
;
Joon Ryang RHO
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Seoul National University, Children's Hospital, Seoul National University College of Medicine, Seoul, Korea. woonghan@snu.ac.kr
- Publication Type:Original Article
- Keywords:
Congenital heart disease;
Pulmonary atresia;
Tricuspid valve
- MeSH:
Blalock-Taussig Procedure;
Echocardiography;
Follow-Up Studies;
Heart Defects, Congenital;
Heart Diseases;
Humans;
Infant, Newborn;
Mortality;
Pulmonary Atresia*;
Tricuspid Valve;
Ventricular Function, Left;
Ventricular Function, Right;
Ventricular Septum*
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2005;38(12):815-820
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
BACKGROUND: Pulmonary atresia with intact ventricular septum is a rare congenital cardiac disease. There have been various surgical options, but there are still controversies. MATERIAL AND METHOD: Fourteen neonates who were operated on between 1999 and 2000 were enrolled in this study. We measured Z-value of tricuspid valve by echocardiography. We performed right ventricular outflow tract transannular patch in 9 patients. Modified Blalock-Taussig shunt was placed according to the condition of patients. Mean follow up period was 46.0 months. RESULT: There were 2 operative mortality and 1 late mortality. Biventricular repair was possible in 7 patients. One and a half ventricular repair were done in 3 (tricuspid valve Z-value was -2, -2.5 and -3) and single ventricular repair in 2 patients (tricuspid z-value was -4.6, -4.5) The tricuspid valve Z-value for the patients who had biventricular repair and one and a half ventricular repair were -0.8+/-1.50 (-3.2~1.2) and -2.5+/-0.5 (-3~-2) respectively. All patients who survived had fair to good right ventricular function, good left ventricular function and good clinical states. CONCLUSION: Neonatal surgical management of pulmonary atresia with intact ventricular septum has a good surgical outcome, z-value of tricuspid may be helpful for the determination of surgical options.
