A Case of Pulmonary Langerhans Cell Histiocytosis associated with Central Diabetes Insipidus in Adult: A case report.
- Author:
Byung Su YOO
1
;
Jae Woong LEE
;
Tae Jun JO
;
Ki Woo HONG
;
Kun Il KIM
;
Weon Yong LEE
;
Dong Gyu KIM
;
Sun Young JUN
Author Information
1. Department of Thoracic and Cardiovascular Surgery, College of Medicine, Hallym University. ljw@hallym.or.kr
- Publication Type:Case Report
- Keywords:
Lung neoplasms;
Histiocytosis;
Diabetes
- MeSH:
Adult*;
Axis, Cervical Vertebra;
Bone Marrow;
Central Nervous System;
Child;
Diabetes Insipidus;
Diabetes Insipidus, Neurogenic*;
Ear;
Gastrointestinal Tract;
Histiocytosis;
Histiocytosis, Langerhans-Cell*;
Humans;
Incidence;
Liver;
Lung;
Lung Neoplasms;
Skin;
Spleen
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2005;38(12):866-869
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Langerhans Cell Histiocytosis (LCH) is a pathologic proliferation and infiltration of various organs by Langerhans' cells of unknown cause. Incidence rate of one million parties 3~4 is seen in young child but the incidence is not sure in adult. Organ systems involved by LCH may include skin, ear, bone marrow, liver, spleen, lung, pituitary gland-hypothalamus and GI tracts. In case pituitary-hypothalamus axis are involved, diabetes insipidus happened. Primary Pulmonary Langerhans Cell Histiocytosis(PLCH) with uninvolvement of other organs is rare and accompanied diabetes insipidus is more rare. There are many cases of LCH with diabetes insipidus involve such as central nervous system except lung. PLCH accompany central diabetes insipidus is only 1 case. We report a case of PLCH that accompany central diabetes insipidus with literature investigation inDepartment of Thoracic and Cardiovascular Surgery, Hallym University.
