A Case of Systemic Vasculitis with Intraperitoneal Aneurysmal Rupture.
- Author:
Beom KIM
1
;
Wooseong HUH
;
Hyun Jeong BAEK
;
Ho Myoung YEO
;
Jung Ah KIM
;
Bang Hoon LEE
;
Yoon Goo KIM
;
Dae Joong KIM
;
Ha Young OH
;
Ghee Young KWON
;
Woo Heon KANG
Author Information
1. Department of Medicine, Sungkyunkwan University School of Medicine, Seoul, Korea. whuh@samsung.co.kr
- Publication Type:Case Report
- Keywords:
Systemic vasculitis;
Polyarteritis nodosa;
Microscopic polyangiitis;
ANCA;
Aneurysmal rupture
- MeSH:
Aneurysm*;
Antibodies, Antineutrophil Cytoplasmic;
Aorta;
Arteritis;
Capillaries;
Cytoplasm;
Glomerulonephritis;
Incidence;
Microscopic Polyangiitis;
Polyarteritis Nodosa;
Prevalence;
Rupture*;
Systemic Vasculitis*
- From:Korean Journal of Nephrology
2004;23(4):655-660
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Though systemic vasculitidis are a group of diseases with extremely low incidence and prevalence, vessels with diverse size from aorta to capillaries are involved. It has been argued how to classify and define systemic vasculitidis, especially how to discriminate poly arteritis nodosa (PAN) and microscopic polyangiitis (MPA). Since there are lots of overlapping between them, clinical manifestations, antineuclear cytoplasmic antibody (ANCA) and angiographic findings besides pathologic findings should be considered altogether. We report a case of systemic vasculitis in which crescentic necrotizing glomerulonephritis with positive perinuclear-type ANCA occurred with intraperitoneal aneurysmal rupture simultaneously. Our case can be a typical one that shows definite overlapping between PAN and MPA.
