Multiple langerhans cell histiocytosis at the lung and mandible: Case report.
- Author:
Jin Hyuk HWANG
1
;
Bu Kyu LEE
Author Information
1. Department of Oral and Maxillofacial Surgery, Asan Medical Center, Seoul, Korea. bukyu67@freechal.com
- Publication Type:Case Report
- Keywords:
Histiocytosis X;
Surgical curettage;
Eosinophilic granuloma
- MeSH:
Eosinophilic Granuloma;
Histiocytes;
Histiocytosis;
Histiocytosis, Langerhans-Cell*;
Liver;
Lung*;
Lymph Nodes;
Mandible*;
Mucous Membrane;
Rare Diseases;
Skin
- From:Journal of the Korean Association of Oral and Maxillofacial Surgeons
2005;31(3):279-282
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hitiocytosis X, recently termed Langergans cell histiocytosis, is a rare disease histologically characterized by an abnormal proliferation of histiocytes, and of which the pathophysiology is still ambiguous. The clinical presentation is highly varied. Typically, there is a solitary or multiple bony involvements, and less frequently, lesions are found in other organs such as the lungs, liver, lymph nodes, skin, and mucosae. Interestingly, so far, there has been no report which shows multiple developments in both soft and hard tissues. In this report, we present a case of hitiocytosis X in both mandible and lung. This may provide some information for understanding the pathophysilogy of the histiocytosis X.
