A Case of Acquired Zonal Aganglionosis in Adult.
- Author:
Woong Jun KIM
1
;
Chang Soo EUN
;
Min Kyu LEE
;
Seung Yeon MIN
;
Yeon Hwa YOO
;
Dong Soo HAN
;
Yong Cheol JEON
;
Joo Hyun SOHN
Author Information
- Publication Type:Case Report
- Keywords: Colonic Pseudo-obstruction; Aganglionosis, Colonic
- MeSH: Adult; Colectomy; Colonic Pseudo-Obstruction; Constipation; Female; Fluconazole; Hirschsprung Disease; Humans; Intestinal Pseudo-Obstruction; Middle Aged
- From:Intestinal Research 2012;10(2):210-214
- CountryRepublic of Korea
- Language:Korean
- Abstract: A chronic intestinal pseudo-obstruction is a rare disorder and a severe digestive syndrome. It is characterized by deranged gut propulsive motility that resembles a mechanical obstruction, but no obstructive process is present. An intestinal pseudo-obstruction may be classified as acute or chronic; the chronic form may also be classified as idiopathic or secondary to a variety of diseases. Treatment of intestinal pseudo-obstruction involves nutritional, pharmacological, and surgical therapies. Surgery should be limited to patients who are refractory to medical therapy and show a deteriorating course. Despite available medical and surgical interventions, the outcome remains poor. Here, we describe a case of a 54-year-old female with chronic constipation and abdominal distension, who was subsequently found to have segmental aganglionosis. The patient was treated with a subtotal colectomy and ileosigmoidostomy without sequelae.
