A Case of Noncompaction of the Ventricular Myocardium Combined with Situs Ambiguous with Polysplenia.
10.3349/ymj.2007.48.6.1052
- Author:
Yun Heyong CHO
1
;
Sung Joon JIN
;
Hyun Chul JE
;
Young Won YOON
;
Bum Kee HONG
;
Hyuck Moon KWON
;
Tae Hoon KIM
;
Se Joong RIM
Author Information
1. Division of Cardiology Yongdong Severance Hospital, Yonsei University College of Medicine, Seoul, Korea. sejoong@yuhs.ac
- Publication Type:Case Report
- Keywords:
Noncompaction of the ventricular myocardium (NVM);
situs ambiguous with polysplenia
- MeSH:
Abnormalities, Multiple/*pathology;
Adult;
Echocardiography;
Heart Ventricles/abnormalities;
Humans;
Magnetic Resonance Imaging;
Male;
Myocardium/*pathology;
Spleen/*abnormalities;
Syndrome;
Tomography, X-Ray Computed
- From:Yonsei Medical Journal
2007;48(6):1052-1055
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 33-year-old man was admitted to our hospital with chest pain and exertional dyspnea. Two-dimensional echocardiography showed prominent trabeculations and deep intertrabecular recesses, findings consistent with noncompaction of the ventricular myocardium. Thoracoabdominal CT and cardiac magnetic resonance imaging (CMR) revealed situs ambiguous with polysplenia and noncompaction of the left ventricular myocardium. CMR also demonstrated delayed enhancement of the trabeculations located at the apical portion of the left ventricle. The coronary angiogram was normal. This is the first case of noncompaction of the ventricular myocardium associated with situs ambiguous with polysplenia.
