Two Cases of Left Ventricular Tumors Complicating Subaortic Stenosis in Newborn Infants.
- Author:
Ji Seon KANG
1
;
Mi Jung HWANG
;
Tae Hyoung CHO
;
Byung Ju KIM
;
Young Jong WOO
;
Jae Sook MA
Author Information
1. Department of Pediatrics, Chonnam National University Medical School, Kwangju, Korea.
- Publication Type:Case Report
- Keywords:
Heart;
Rhabdomyoma;
Subaortic stenosis;
Tuberous sclerosis
- MeSH:
Aortic Valve;
Constriction, Pathologic*;
Diagnosis;
Echocardiography;
Follow-Up Studies;
Heart;
Heart Neoplasms;
Heart Ventricles;
Humans;
Hypertrophy;
Infant, Newborn*;
Rhabdomyoma;
Tuberous Sclerosis;
Ventricular Septum
- From:Journal of the Korean Pediatric Society
2000;43(8):1122-1126
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The most cornmon obstruction of left ventricular outflow in childhood is produced either by a fibrous ring below the aortic valve, or by localized or diffuse muscular hypertrophy of the inter-ventricular septum. Cardiac tumors causing subaortic stenosis in the newborn infant are extremely rare. This report describes two cases of subaortic stenosis caused by a tumor of the left ventricle in newborn infants, both diagnosed by 2-dimensional echocardiography. In one patient, the obstructive portion of the tumor was successfully resected from its attachment to the ventricular septum by aortotomy on day 5. Histologic examination confirmed the diagnosis of rhabdomyoma. This patient developed cutaneous, neurologic and radiologic abnormalities of tuberous sclerosis during the follow-up of 42 months.
