A case of Von Meyenburg Complex associated with calculous cholecystitis, cerebral aneurysm and renal cortical cyst.
- Author:
Se Haeng CHO
1
;
Chan Ho OCK
;
Choon Woong HUH
;
Il Joo YOON
;
Hyung Sim SUH
;
Sung Nam KIM
Author Information
1. Department of Internal medicine, Myung-Ji St.mary's Hospital, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Von meyenburg complex;
Bile duct hamartoma;
MRCP
- MeSH:
Bile Ducts;
Cholecystitis*;
Diagnosis;
Hamartoma;
Intracranial Aneurysm*;
Magnetic Resonance Imaging;
Ultrasonography
- From:Korean Journal of Medicine
2001;60(4):388-392
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Von Meyenburg complexes (VMC) have many synonyms such as bile duct hamartomas and biliary hamartoma. These rare benign disorders are considered as congenital diseases caused by malformed differentiation of ductal plate. The diagnosis of VMC by common radiologic modality such as ultrasound and computed tomography was nearly impossible until the emergence of cholangiopancreatography by magnetic resonance imaging (MRCP) and the pathologic examination was the only way to confirm the diagnosis of VMC. But MRCP is now considered as most accurate noninvasive method for diagnosis of VMC. We report a histologically proven case of VMC associated with calculous cholecystitis, cerebral aneurysm and renal cortical cyst. To our knowledge, no comparable case has been reported and this would be the only second reported case of VMC, which was diagnosed by MRCP.
