Two Cases of Microscopic Polyangiitis with Honeycomb Lung.
10.4046/trd.2002.52.5.550
- Author:
Hye Sook HAHN
1
;
Jun Kyu HWANG
;
Hyuk Sang JUNG
;
Suk Ho SONG
;
Kwon Wook JOO
;
Gye Young PARK
;
Jong Ho LEE
;
Young Ha OH
;
Hyoun Joo LEE
Author Information
1. Department of Internal Medicine, Gachon Medicial School, Gil Medical Center, Inchon, Korea. jookw@ghil.com
- Publication Type:Case Report
- Keywords:
Microscopic polyangiitis;
Honeycomb lung;
Idiopathic pulmonary fibrosis
- MeSH:
Diagnosis;
Glomerulonephritis;
Hemorrhage;
Humans;
Idiopathic Pulmonary Fibrosis;
Lung Diseases, Interstitial;
Lung*;
Microscopic Polyangiitis*;
Vasculitis
- From:Tuberculosis and Respiratory Diseases
2002;52(5):550-556
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Microscopic polyangiitis is a systemic small-vessel vasculitis that is associated primarily with necrotizing glomerulonephritis and pulmonary capillaritis. A recurrent and diffuse alveolar hemorrhage due to pulmonary capi llaritis is the main clinical manifestation of lung involvement. Recently, an interstitial lung disease that mimics idiopathic pulmonary fibrosis was reported to be rarely associated with microscopic polyangiitis. Here we report two patients with microscopic polyangiitis who showed a honeycomb lung at the time of the initial diagnosis with a brief review of relevant literature.