Catastrophic Antiphospholipid Syndrome Improved by Anticoagulation Alone.
- Author:
Yoon Jeong KIM
1
;
Seouk Chan KO
;
Sung Du KIM
;
Ho Jun LEE
;
Myung Jae YUN
;
Su Hyun KIM
;
Na Ree KANG
Author Information
1. Department of Internal Medicine, Seoul Medical Center, Seoul, Korea. narikg@hanmail.net
- Publication Type:Case Report
- Keywords:
Antiphospholipid syndrome;
Pathophysiology;
Therapy
- MeSH:
Adrenal Cortex Hormones;
Antiphospholipid Syndrome;
Immunoglobulins;
Korea;
Plasma Exchange;
Steroids
- From:Korean Journal of Medicine
2011;80(Suppl 2):S319-S324
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Catastrophic antiphospholipid syndrome (APS) is an accelerated subtype of APS that results in multiorgan failure. Although catastrophic APS represents about 0.8% of all APS cases, it is usually a life-threatening medical condition that requires high clinical awareness. Catastrophic APS has been managed by various therapies, including anticoagulation, corticosteroids, plasma exchange and IV immunoglobulin, but it still has a high mortality rate. A few cases treated by anticoagulation and steroids have been reported in Korea. In this paper, we report a case of catastrophic APS that improved after anticoagulation therapy alone. Thus, we consider hat our case shows another clinical aspect of catastrophic APS.