A Case of Primary Autoimmune Myelofibrosis.
- Author:
Yeongmin LIM
1
;
Chi Young PARK
;
Won Jung HONG
;
Gwangil KIM
;
Soyoung CHONG
;
Doyeun OH
Author Information
1. Department of Internal Medicine, School of Medicine, CHA University, Seongnam, Korea. doh@cha.ac.kr
- Publication Type:Case Report
- Keywords:
Primary autoimmune myelofibrosis;
Leukoerythroblastosis;
Prednisolone
- MeSH:
Aged;
Autoantibodies;
Autoimmune Diseases;
Female;
Humans;
Pancytopenia;
Prednisolone;
Primary Myelofibrosis*
- From:Korean Journal of Medicine
2014;86(5):632-636
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary autoimmune myelofibrosis, the development of which is not preceded by a well-defined autoimmune disease, has recently been defined as a distinct clinicopathologic syndrome. We report herein a case of a 68-year-old woman who was diagnosed with primary autoimmune myelofibrosis and present a review of the literature. The patient manifested peripheral pancytopenia, was positive for autoantibodies, and developed myelofibrosis with no preceding autoimmune or hematologic disorders. Her condition was dramatically improved after administration of prednisolone.
