Classical malignant rhabdoid tumor of central nervous system in 9-year-old Korean.
10.3349/ymj.2001.42.1.142
- Author:
Hee Kyung CHANG
1
;
Jung H KIM
Author Information
1. Department of Pathology, Medical College of Kosin University, Pusan, Korea. changhkg@ns.kosinmed.or.kr
- Publication Type:Case Report
- Keywords:
malignant rhabdoid tumor;
atypical teratoid/rhabdoid tumor;
central nervous system;
immunohistochemistry;
9-year-old boy
- MeSH:
Brain Neoplasms/therapy;
Brain Neoplasms/pathology;
Brain Neoplasms/metabolism*;
Case Report;
Child;
Glial Fibrillary Acidic Protein/analysis;
Human;
Immunohistochemistry;
Male;
Rhabdoid Tumor/therapy;
Rhabdoid Tumor/pathology;
Rhabdoid Tumor/metabolism*;
Vimentin/analysis
- From:Yonsei Medical Journal
2001;42(1):142-146
- CountryRepublic of Korea
- Language:English
-
Abstract:
A Malignant rhabdoid tumor (MRT) arising in the right temporoparietal lobe of a 9-year-old boy is described along with the results of an immunohistochemical study. The patient initially sought medical attention for a ptosis and right sided headache. The child underwent a subtotal resection of the tumor, followed by radiotherapy and systemic chemotherapy, but died three years after surgery. A MRT, a primary neoplasm of the central nervous system (CNS), is an entity of unknown histogenesis with a dismal prognosis, which only occurs in early childhood. Histologically similar tumors with more varied morphological features have been designated as an atypical teratoid/rhabdoid tumor. However, a classical MRT is extremely rare in the CNS and our case represents a classical CNS MRT.
