General anesthesia for a spinal muscular atrophy type I patientundergoing feeding gastrostomy: A case report.
- Author:
Eun Ho JANG
1
;
Kwang Rae CHO
;
Hyun Tae KIM
;
Se Hun LIM
;
Jeong Han LEE
;
Kun Moo LEE
;
Soon Ho CHEONG
;
Young Jae KIM
;
Chee Mahn SHIN
Author Information
1. Department of Anesthesiology and Pain Medicine, Paik Hospital, College of Medicine, Inje University, Busan, Korea. maeteo@hanmir.com
- Publication Type:Case Report
- Keywords:
Gastrostomy;
Neuromuscular disease;
Spinal muscular atrophy type I
- MeSH:
Anesthesia;
Anesthesia, General;
Child;
Deglutition Disorders;
Female;
Gastrostomy;
Humans;
Infant;
Muscle Weakness;
Muscles;
Muscular Atrophy, Spinal;
Neuromuscular Diseases;
Pneumonia, Aspiration;
Spinal Muscular Atrophies of Childhood
- From:Anesthesia and Pain Medicine
2010;5(4):329-332
- CountryRepublic of Korea
- Language:English
-
Abstract:
Spinal muscular atrophy (SMA) in children leads to progressive muscle weakness, dysphagia, aspiration, and death. The most common and severe form of SMA is designated as type I, also known as Werdnig-Hoffman Disease or Floppy Baby syndrome. We anesthetized an 8 month-old female infant with SMA type I undergoing feeding gastrostomy. We planned to use inhalational anesthesia without muscle relaxants. Anesthesia and surgery were uneventful. We herein report a case of successful peri-operative anesthetic management for SMA type I infant with aspiration pneumonia.
