Total Intravenous Anesthetic Management of a Child with Congenital Insensitivity to Pain with Anhidrosis : A case report.
10.4097/kjae.2007.52.3.367
- Author:
Seuk Jin LEE
1
;
Young Ki KIM
;
Kyu Wan SEONG
;
Seong Woo KIM
Author Information
1. Department of Anesthesiology and Pain Medicine, Gangneung Asan Hospital, University of Ulsan College of Medicine, Gangneung, Korea. ykkim@gnah.co.kr
- Publication Type:Case Report
- Keywords:
congenital insensitivity to pain with anhidrosis;
propofol;
remifentanil;
total intravenous anesthesia
- MeSH:
Anesthesia;
Anesthesia, Intravenous;
Autonomic Nervous System;
Child*;
Hereditary Sensory and Autonomic Neuropathies*;
Humans;
Intellectual Disability;
Osteomyelitis;
Pain Insensitivity, Congenital*;
Propofol;
Sweat
- From:Korean Journal of Anesthesiology
2007;52(3):367-370
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare hereditary sensory and autonomic neuropathy. CIPA is characterized by inability to sweat, insensitivity to pain, self-mutilation, recurrent episodes of hyperpyrexia, mental retardation, and autonomic nervous system abnormality. Patients with CIPA may undergo surgery because of susceptibility to trauma, bony fracture and osteomyelitis due to insensitivity to pain. We report a child who had undergone anesthesia with total intravenous anesthesia. The anesthetic management of this condition is discussed.