Dandy-Walker Malformation Associated with Neurocutaneous Melanosis.
10.3340/jkns.2011.50.5.475
- Author:
In Yong CHO
1
;
Sung Kyun HWANG
;
Sung Hak KIM
Author Information
1. Department of Neurosurgery, College of Medicine, Ewha Womans University, Seoul, Korea. shsg@ewha.ac.kr
- Publication Type:Case Report
- Keywords:
Dandy-Walker malformation;
Neurocutaneous melanosis;
Hydrocephalus
- MeSH:
Central Nervous System;
Dandy-Walker Syndrome;
Humans;
Hydrocephalus;
Infant;
Melanosis;
Neurocutaneous Syndromes;
Nevus
- From:Journal of Korean Neurosurgical Society
2011;50(5):475-477
- CountryRepublic of Korea
- Language:English
-
Abstract:
Neurocutaneous melanosis associated with Dandy-Walker malformation is a rare dysmorphogenesis that is associated with single or multiple giant pigmented cutaneous nevi and diffuse involvement of the central nervous system. In this article, we present a 2-month-old patient with neurocutaneous melanosis associated with Dandy-Walker malformation. In addition, we reviewed the literature and discussed the pathogenesis based on the preferred hypotheses.
