A Case of Woringer - Kolopp Disease ( Pagetoid Reticulosis ).
- Author:
Sang Cheul EOM
;
Yun Kyew KIM
;
Young Soo CHAE
;
Kee Suck SUH
;
Sang Tae KIM
- Publication Type:Case Report
- Keywords:
Electron Beam Theapy;
Woringer-Kolopp Disease
- MeSH:
Epidermis;
Extremities;
Follow-Up Studies;
Foot;
Humans;
Lymphoproliferative Disorders;
Male;
Middle Aged;
Mycosis Fungoides;
Pagetoid Reticulosis*;
Skin
- From:Korean Journal of Dermatology
1994;32(1):119-123
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Woringer-Kolopp(W-K) disease is a rare, localized, histologically malignant, but clinically indolent lymphoproliferative disorder. It usually shows only a single slowly enlarging skin lesion mainly on the extremities. Some authors have regarded W-K disease as a variant of mycosis fungoides. However, recent studies suggest that W-K disease may represent a spectrum of T cell lymphoproliferative disoreers that may not be related to mycosis fungoides. We report a case of Woringer-Kolopp disease in a 60-year-old male who presented with a solitary slowly growing tumor on his left palm for 3 years. Histopathologic examination showed marked acanthosis and pagetoid infiltration confined to the epidermis. He was treated with 4,000 red electron beam irradiation to the area with complete resolution of the lesion. Three years later, a similar lesion appeared on his left foot dorsum. He was treated as previously with a good response and there has been no new lesion during the last 1 year follow up period.
