A Case of Biliary Atresia with Ileal Atresia.
- Author:
So Yeon KIM
1
;
Hyun Jung NA
;
Woo Taek KIM
;
Woo Hyun PARK
;
Jin Kyung KIM
Author Information
1. Department of Pediatrics, College of Medicine, The Catholic University of Korea. kimjk@cu.ac.kr
- Publication Type:Case Report
- Keywords:
Biliary;
Ileal;
Atresia
- MeSH:
Bile;
Biliary Atresia*;
Cardiovascular System;
Gastrointestinal Tract;
Gene Expression;
Jaundice;
Spleen
- From:Korean Journal of Pediatrics
2004;47(8):908-911
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Biliary atresia is a progressive obliterative cholangiopathy. However, the actual causes remain unknown, although a number of factors such as developmental malformation, viral infection, toxicity of bile constituents, and anatomic abnormality in the hepatobiliary system have been considered. Recently, several studies have been done to find out specific gene expression. Some cases of biliary atresia are associated with anomalies of cardiovascular system, digestive tract and spleen. Few cases of biliary atresia with congenital ileal atresia were reported. We experienced a case with biliary atresia combined with ileal atresia. Ileal resection and end to end anastomosis operation were done at second days of the life because of congenital ileal atresia. Jaundice and acholic stool were noticed a few days after the operation. He was diagnosed as biliary atresia and received Kasai operation at 23 days of the life. Therefore, we report the case with a brief review of the related literature.