Pachydermoperiostosis Accompanied by Heart Failure.
10.4250/jcu.2009.17.4.135
- Author:
Kwen Chul SHIN
1
;
Wook Jin CHUNG
;
Ki Young LEE
;
Mi Seung SHIN
;
Sei Hyun KIM
;
Yun Jeong JO
;
Yae Min PARK
;
Tae Hoon AHN
;
In Suk CHOI
;
Eak Kyun SHIN
Author Information
1. Division of Cardiology, Department of Internal Medicine, Gachon University Gil Hospital, Incheon, Korea. heart@gilhospital.com
- Publication Type:Case Report
- Keywords:
Heart failure;
Systolic;
Echocardiography;
Primary hypertrophic osteoarthropathy
- MeSH:
Echocardiography;
Hand;
Heart;
Heart Failure;
Leg;
Osteoarthropathy, Primary Hypertrophic;
Osteogenesis;
Phenotype;
Skin
- From:Journal of Cardiovascular Ultrasound
2009;17(4):135-137
- CountryRepublic of Korea
- Language:English
-
Abstract:
Pachydermoperiostosis or primary hypertrophic osteoarthropathy is an uncommon disease of acromegaloid facial feature, but characterized by unique phenotype (digital clubbing and pachydermia) and distinctive radiographic appearances like periostosis. We experienced a case with complete form of pachydermoperiostosis accompanied by heart failure. He presented with typical features consisting of clubbing with enlargement of the hand, thickening of facial skin and periosteal new bone formation involving lower leg. Echocardiography revealed severely decreased left ventricular systolic function. Treatment with medications resulted in an improvement of cardiac function and symptom. There is no previous report documenting pachydermoperiostosis accompanied by heart failure. We report that case for the first time.
