Infantile Type Choledochal Cyst with Biliary Atresia: Report of two cases.
- Author:
Eun Young KIM
1
;
Seung Hoon HAHN
;
So Young KIM
;
In Kyung SUNG
;
Won Bae LEE
;
Chung Sik CHUN
;
Gye Yeon LIM
;
Chan Kun JUNG
Author Information
1. Department of Pediatrics, College of Medicine, Catholic University, Seoul, Korea. sykim@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Choledochal Cyst;
Biliary Atresia;
Infant
- MeSH:
Bile Ducts, Extrahepatic;
Biliary Atresia*;
Choledochal Cyst*;
Choledochostomy;
Cholestasis;
Humans;
Infant;
Infant, Newborn;
Prognosis
- From:Journal of the Korean Society of Neonatology
2007;14(2):226-231
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Choledochal cysts in neonates and young infants take two forms: the choledochal cyst associated with biliary atresia (CCBA) and the choledochal cyst in the absence of biliary atresia (CC). Infants in both groups usually have similar clinical symptoms at presentation, but management and prognosis are different. While early portoenterostomy is required for CCBA, cyst excision with hepaticojejunostomy or choledochojejunostomy is usually performed for CC. The former shows a relatively poor prognosis, and the latter shows a better prognosis. Two infants who presented with clinical features of neonatal cholestasis, and clinically suspected to have choledochal cysts, were found on imaging studies and surgery to have extrahepatic bile duct atresia in association with choledochal cysts.