Malignant Solitary Fibrous Tumor in the Perianal Region.
- Author:
Yoon SI
1
;
Hyung Jin KIM
;
Won Kyung KANG
;
Chan Kwon JUNG
;
Seong Taek OH
Author Information
1. Department of Surgery, College of Medicine, The Catholic University of Korea, Seoul, Korea. stoh@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Malignant solitary fibrous tumor;
Perianal region
- MeSH:
Collagen;
Desmin;
Humans;
Magnetic Resonance Imaging;
Middle Aged;
Necrosis;
Pleura;
Solitary Fibrous Tumors*
- From:Journal of the Korean Surgical Society
2007;73(5):443-446
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Solitary fibrous tumors (SFT) are rare spindle-cell neoplasms that are found principally in the pleura, and extrathoracic SFTs are even less common. We report here on a case of malignant solitary fibrous tumor in the perianal region. A 47-year-old man was referred to our hospital for surgical treatment of an incidentally discovered perianal mass. Pelvic MRI showed a slightly lobulated solid mass with central necrosis in the ischiorectal fossa. We performed complete removal of tumor with using a postanal approach. The resected specimen was 6.5x5.0x5.0 cm in size, and it was an elastic solid tumor with invasion to the surrounding muscle structures. Histologically, the tumor was composed of a patternless proliferation of spindle cells with a collagenous matrix and the tumor cells showed increased cellularity, cellular pleomorphism and frequent mitotic figure. Immunohistochemical staining was positive for CD34 and negative for desmin, which indicated malignant SFT. We report here on a rare case of malignant SFT in the perianal region along with a review of the literature.
