Clinical manifestations and anesthetic management of Kearns-Sayre syndrome: A case report.
- Author:
Hae Mi LEE
1
;
Su Jeong HEO
;
Dae Lim JEE
Author Information
1. Department of Anesthesiology and Pain Medicine, School of Medicine, Yeungnam University, Daegu, Korea. adjee@medical.yeungnam.ac.kr
- Publication Type:Case Report
- Keywords:
General anesthesia;
Kearns-Sayre syndrome;
Mitochondrial disease
- MeSH:
Adolescent;
Anesthesia;
Anesthesia, General;
Heart Block;
Humans;
Kearns-Sayre Syndrome;
Laryngeal Masks;
Methyl Ethers;
Mitochondrial Diseases;
Muscle Relaxation;
Muscles;
Thiopental
- From:Anesthesia and Pain Medicine
2011;6(3):290-293
- CountryRepublic of Korea
- Language:English
-
Abstract:
Kearns-Sayre syndrome (KSS) is a mitochondrial disorder resulting in multi-system dysfunction. A 14-year-old boy with KSS underwent external levator muscle resection for correction of ptosis. There were no abnormalities on the pre-operative evaluation, except for low-grade heart block and ocular problems. General anesthesia was conducted with a minimum dose of thiopental sodium and sevoflurane under close monitoring, and a laryngeal mask was inserted without muscle relaxation. The surgery was uneventful; however, a careful approach was required during anesthesia because life-threatening complications may occur in patients with KSS.
