Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney.
10.4111/kju.2013.54.3.209
- Author:
Sunchan KIM
1
;
Tae Gu KIM
;
Seung Kwon CHOI
;
Myung Joon KIM
;
Gyeong Eun MIN
;
Hyung Lae LEE
;
Koo Han YOO
Author Information
1. Department of Urology, Kyung Hee University Hospital at Gangdong, Seoul, Korea. yookoohan@yahoo.co.kr
- Publication Type:Case Report
- Keywords:
Immunoglobulin G;
Sclerosis;
Ureter
- MeSH:
Adrenal Cortex Hormones;
Fibrosis;
Humans;
Immunoglobulin G;
Immunoglobulins;
Kidney;
Plasma Cells;
Sclerosis;
Ureter
- From:Korean Journal of Urology
2013;54(3):209-211
- CountryRepublic of Korea
- Language:English
-
Abstract:
Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.
