A Case of Bilateral Anterior Opercular Syndrome: Foix-Chavany-Marie Syndrome.
- Author:
Dong Eog KIM
1
;
Yong Seok LEE
;
Seong Ho PARK
;
Kyung Il PARK
;
Joong Yang CHO
;
Sam Soo KIM
;
Hyun Woo NAM
;
Kwang Woo LEE
;
Jae Kyu ROH
Author Information
1. Department of Neurology, Seoul Municipal Boramae Hospital.
- Publication Type:Case Report
- Keywords:
Bilateral anterior opercular syndrome;
Foix-Chavany-Marie syndrome;
Operculum;
Automatic-voluntary dissociation
- MeSH:
Apraxias;
Brain;
Constriction, Pathologic;
Cues;
Deglutition;
Deglutition Disorders;
Diagnosis, Differential;
Hemiplegia;
Humans;
Jaw;
Korea;
Mastication;
Middle Aged;
Middle Cerebral Artery;
Mouth;
Pseudobulbar Palsy;
Reflex;
Rehabilitation
- From:Journal of the Korean Neurological Association
2000;18(4):450-453
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Bilateral opercular syndrome or Foix-Chavany-Marie syndrome (FCMS) is characterized by facio-pharyngo-glosso-masticatory diplegia with an automatic-voluntary movement dissociation, which is usually caused by bilateral fron-toparietal opercular lesions. A 52 year-old man suddenly developed left hemiplegia and also presented with anarthria, dysphagia, difficulty in jaw opening and mastication. However, involuntary swallowing and slight control of jaw move-ments were partly preserved. His gag reflex was decreased and emotional incontinence was absent. Brain magnetic res-onance (MR) imaging revealed high signal lesions in the right middle cerebral artery territory and left anterior opercu-lum. Severe stenosis of the right middle cerebral artery was observed on a MR angiogram. Rehabilitation training by cueing has improved his ability to open the mouth. To our knowledge, this is the first report of FCMS in Korea, and a cautious differential diagnosis of pseudobulbar palsy or buccofacial apraxia may be crucial.
