An anesthetic experience in a patient with Seckel syndrome: A case report.
10.4097/kjae.2009.56.2.204
- Author:
Jong Bum CHOI
1
;
Seung Youn KANG
;
Hae Keum KIL
Author Information
1. Department of Anesthesiology and Pain Medicine, Yonsei University College of Medicine, Seoul, Korea. hkkil@yuhs.ac
- Publication Type:Case Report
- Keywords:
Dwarfism;
Endotracheal intubation;
Nanocephaly;
Seckel syndrome
- MeSH:
Curettage;
Dwarfism;
Humans;
Intellectual Disability;
Intubation, Intratracheal;
Laryngoscopes;
Nose;
Osteomyelitis;
Pelvic Bones
- From:Korean Journal of Anesthesiology
2009;56(2):204-207
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Seckel syndrome is an autosomal recessive, primordial dwarfism. The clinical symptoms and signs include severe intrauterine and postnatal growth retardation, nanocephaly, proportional dwarfism, bird-like faces, beak-like triangular nose, and mental retardation. We report a successful anesthetic management including endotracheal intubation with the GlideScope(R) video laryngoscope in an 18-year old man with Seckel syndrome for curettage of chronic osteomyelitis of pelvic bone.