Anesthetic managements for repair of atrial septal defect in a patient with Young-Simpson Syndrome: A case report.
10.4097/kjae.2009.56.2.225
- Author:
Seong Hyop KIM
1
;
Tae Yop KIM
;
Hwa Sung JUNG
;
Joo eun KANG
;
Chung Sik OH
;
Duk Kyung KIM
;
Tae Gyoon YOON
Author Information
1. Department of Anesthesiology and Pain Medicine, School of Medicine, Konkuk University, Seoul, Korea. pondkim@unitel.co.kr
- Publication Type:Case Report
- Keywords:
Young-Simpson Syndrome
- MeSH:
Blepharophimosis;
Congenital Hypothyroidism;
Facies;
Heart Defects, Congenital;
Heart Septal Defects, Atrial;
Humans;
Infant;
Intellectual Disability;
Joint Instability
- From:Korean Journal of Anesthesiology
2009;56(2):225-229
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Young-Simpson Syndrome (YSS) is a rare malformation syndrome characterized by facial dysmorphism, congenital heart abnormalities, congenital hypothyroidism and severe growth retardation. A 5-month-old girl was scheduled to undergo patch closure of atrial septal defect. She had been diagnosed with YSS preoperatively. We report out clinical experience of a case of YSS patient with brief review of related literatures and relevant anesthetic problems.
